PW01-030 – Pulmonary manifestations of FMF
نویسندگان
چکیده
Methods The study cohort involved 155 FMF patients (male/female 87/68). Mean age was 33,6±11,8 years in the patients group without renal amyloidosis (45 men, 35 women, n=80) and 37,8±7,4 years in the patients group with amyloidosis (42 men, 33 women, n=75). All the patients had symptoms related to the respiratory system, such as pleuritic chest pain with or without cough, dyspnea, chest tightness and frequent pneumonias. 28 patients had a history of tobacco use. Most of the patients (122) had M694V mutation, and the rest had other mutations. All the patients were on colchicine treatment at the time of the study with the exception of 2 hemodialysis patients. Laboratory tests, including CRP, SAA and capillary blood gases, ECG and chest X-ray were carried out on all the patients. 50 patients underwent Doppler echocardiography and 25 HRCT scan of the chest.
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